| CASE REPORT |
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| Year : 2021 | Volume
: 10
| Issue : 1 | Page : 42-44 |
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A rare and curable cause of cyanosis – Congenital portosystemic shunts
Balasubramaniyan Amirtha Ganesh DNB , Arumugam Aashish DM , Selvaraj Karthikeyan DM , Srinivasan Giridharan DM
Department of Cardiology, Mahatma Gandhi Medical College and Research Institute, Puducherry, India
Correspondence Address:
Dr. Balasubramaniyan Amirtha Ganesh
Department of Cardiology, Mahatma Gandhi Medical College and Research Institute, 1st Floor, E Block, Puducherry
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/JCPC.JCPC_50_20
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Congenital portosystemic shunts (CPSSs) are rare developmental vascular anomalies which are classified into extrahepatic and intrahepatic malformations. Here, we report a 7-year-old girl who presented with a history of progressive dyspnea, pandigital cyanosis, and clubbing. On evaluation, she was found to have a rare combination of both type II extrahepatic and intrahepatic portosystemic shunts which were closed endovascularly in the same setting. Diagnosis of CPSS needs a very high index of clinical suspicion. Timely diagnosis with specific imaging modalities will help in deciding the treatment strategy and may prevent long-term complications.
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