Journal of Clinical and Preventive Cardiology

CASE REPORT
Year
: 2021  |  Volume : 10  |  Issue : 1  |  Page : 42--44

A rare and curable cause of cyanosis – Congenital portosystemic shunts


Balasubramaniyan Amirtha Ganesh, Arumugam Aashish, Selvaraj Karthikeyan, Srinivasan Giridharan 
 Department of Cardiology, Mahatma Gandhi Medical College and Research Institute, Puducherry, India

Correspondence Address:
Dr. Balasubramaniyan Amirtha Ganesh
Department of Cardiology, Mahatma Gandhi Medical College and Research Institute, 1st Floor, E Block, Puducherry
India

Congenital portosystemic shunts (CPSSs) are rare developmental vascular anomalies which are classified into extrahepatic and intrahepatic malformations. Here, we report a 7-year-old girl who presented with a history of progressive dyspnea, pandigital cyanosis, and clubbing. On evaluation, she was found to have a rare combination of both type II extrahepatic and intrahepatic portosystemic shunts which were closed endovascularly in the same setting. Diagnosis of CPSS needs a very high index of clinical suspicion. Timely diagnosis with specific imaging modalities will help in deciding the treatment strategy and may prevent long-term complications.


How to cite this article:
Ganesh BA, Aashish A, Karthikeyan S, Giridharan S. A rare and curable cause of cyanosis – Congenital portosystemic shunts.J Clin Prev Cardiol 2021;10:42-44


How to cite this URL:
Ganesh BA, Aashish A, Karthikeyan S, Giridharan S. A rare and curable cause of cyanosis – Congenital portosystemic shunts. J Clin Prev Cardiol [serial online] 2021 [cited 2023 Mar 30 ];10:42-44
Available from: https://www.jcpconline.org/article.asp?issn=2250-3528;year=2021;volume=10;issue=1;spage=42;epage=44;aulast=Ganesh;type=0